Courses
Movement Disorders
Cortical Tremor
Hereditary Essential Myoclonus (Myoclonus Dystonia)
Lance-Adams syndrome
Progressive Myoclonic Epilepsies
Propriospinal Myoclonus
Myoclonus
INDEX
1
Overview of Myoclonus
2
Classification of Myoclonus
3
Examination of Myoclonus
3.1
Activating Condition
3.2
Location
3.3
Severity
3.4
Writing and Drawing
3.5
Associated Movements/Neurology
4
Physiology of Myoclonus
4.1
EMG burst length
4.2
Somatosensory Evoked Potential
4.3
Transcortical C-reflex
4.4
Jerk-locked Back-Averaging
5
Anatomy of Myoclonus
6
Rating Scales
7
Differential Diagnosis
7.1
Cortical Tremor
7.2
Lance-Adams syndrome
7.3
Acute Post-hypoxic myoclonus
7.4
Orthostatic Myoclonus
7.5
PME
7.5.1
Unverricht-Lundborg Disease
7.5.2
Lafora Body Disease
7.5.3
Mitochondrial Disease
7.5.4
NCL
7.5.5
DRPLA
7.5.6
FAME
7.5.7
Sialidoses
7.5.8
Gaucher Disease
7.5.9
GM2 Gangliosidoses
7.5.10
Coeliac Disease
7.6
Essential Myoclonus (Myoclonus Dystonia)
7.7
Propriospinal Myoclonus
7.8
Spinal (Segmental) Myoclonus
7.9
Subcortical Myoclonus
7.10
Functional Myoclonus
Activating Condition
References